Coats disease

Coats disease is also known as Coats' disease, retinal telangiectasis, unilateral retinal telangiectasis, idiopathic retinal telangiectasia, primary (congenital) retinal telangiectasia, OMIM 300216.

It is a sporadic idiopathic disorder characterized by abnormal retinal vascular development (retinal telangiectasis) that results in vessel leakage, subretinal exudation, and retinal detachment.

Severity can range from slight vision loss to total retinal detachment and blindness. Coats disease belongs to the group of vitreoretinal dystrophies and was first reported by G. Coats in 1908.